Review Article

National Consensus on Diagnosis and Management Guidelines for Primary Immunodeficiency

Abstract


Primary immunodeficiency (PID) is a group of more than 400 distinct genetic disorders affecting both children and adults. As signs and symptoms of PID are usually heterogeneous and unspecific, diagnosis and follow-up of these patients can be challenging based on the available human resources and laboratory facilities. In order to reach a distinct national protocol and due to little evidence to guide appropriate or universal guidelines to improve the current status of management of the disease, the Iranian PID network designed a consensus appropriate for regional resources. This review summarizes this PID guideline based on the importance of different clinical complications and the level of medical authority visiting those at the first line. Moreover, for each complication, appropriate interventions for improving approach are mentioned.
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IssueVol 2, No 1 (2019) QRcode
SectionReview Article
DOI https://doi.org/10.22034/igj.2019.85743
Keywords
Primary immunodeficiency Symptoms Management consensus guideline
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How to Cite
1.
Abolhassani H, Tavakol M, Chavoshzadeh Z, Mahdaviani SA, Momen T, Yazdani R, Azizi G, Movahedi M, Hamidieh AA, Behniafard N, Nabavi M, Arshi S, Bemanian MH, Fallahpour M, Shokri S, Molatefi R, Sherkat R, Shirkani A, Amin R, Aleyasin S, Faridhosseini R, Jabbari-Azad F, Mohammadzadeh I, Ghaffari J, Shafiei A, Kalantari A, Mansouri M, Mesdaghi M, Babaie D, Ahanchian H, Khoshkhui M, Soheili H, Eslamian MH, Cheraghi T, Dabbaghzadeh A, Tavassoli M, Nasiri Kalmarzi R, Mortazavi SH, Kashef S, Esmaeilzadeh H, Tafaroji J, Khalili A, Zandieh F, Sadeghi-Shabestari M, Darougar S, Behmanesh F, Akbari H, Zandkarimi M, Abolnezhadian F, Fayezi A, Moghtaderi M, Ahmadiafshar A, Shakerian B, Sajedi V, Taghvaei B, Safari M, Heidarzadeh M, Ghalehbaghi B, Fathi SM, Darabi B, Bazregari S, Bazargan N, Khayatzadeh A, Javahertrash N, Bashardoust B, Zamani M, Mohsenzadeh A, Ebrahimi S, Sharafian S, Vosughimotlagh A, Tafakoridelbari M, Rahimi M, Ashournia P, Razaghian A, Aghaeimeybodi F, Mamishi S, Parvaneh N, Rezaei N, Aghamohammadi A. National Consensus on Diagnosis and Management Guidelines for Primary Immunodeficiency. Immunol Genet J. 2019;2(1):1-21.